ICD-10 code for acantholytic disorder

The ICD-10-CM code for acantholytic disorder is L11.9 (Acantholytic disorder, unspecified). The official index lists 1 more specific code, so check the documentation for details such as type, cause, site or severity before settling on L11.9.

Within L11, choose L11.9 (Acantholytic disorder, unspecified) only when documentation doesn't support a more specific option: acquired keratosis follicularis (L11.0), transient acantholytic dermatosis [Grover] (L11.1) and other specified acantholytic disorders (L11.8).

It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.

In MS-DRG v44.0, it is part of the grouping logic for DRG 606 (Minor Skin Disorders with MCC, relative weight 1.5728) and DRG 607 (Minor Skin Disorders without MCC, relative weight 0.8772), in MDC 09 (Diseases and Disorders of the Skin, Subcutaneous Tissue and Breast), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.