ICD-10-CM 2027
ICD-10 code for Achalasia
From the official ICD-10-CM alphabetic index entry “Achalasia (cardia) (esophagus)”. Page updated September 29, 2026.
About coding Achalasia
The ICD-10-CM code for Achalasia is K22.0 (Achalasia of cardia). The official index lists 3 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on K22.0.
Within K22 (other diseases of esophagus), K22.0 is specifically for Achalasia of cardia. Related codes cover ulcer of esophagus (K22.1), esophageal obstruction (K22.2), perforation of esophagus (K22.3), dyskinesia of esophagus (K22.4), diverticulum of esophagus, acquired (K22.5), Gastro-esophageal laceration-hemorrhage syndrome (K22.6), Barrett's esophagus (K22.7), other specified diseases of esophagus (K22.8) and 1 more.
Don't report K22.0 together with the conditions in its Excludes1 note: congenital cardiospasm (Q39.5).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
More specific Achalasia codes (official index)
Don't confuse with (Excludes1 for K22.0)
- congenital cardiospasm (Q39.5)
Common questions about Achalasia ICD-10 codes
What is the ICD-10 code for Achalasia?
- K22.0 — Achalasia of cardia. More specific codes apply when the documentation supports them: Q39.5, Q40.0, K59.89.
What is the ICD-10 code for congenital achalasia?
- Q39.5 — Congenital dilatation of esophagus.
What is the ICD-10 code for pylorus achalasia?
- Q40.0 — Congenital hypertrophic pyloric stenosis.
What is the ICD-10 code for sphincteral nec achalasia?
- K59.89 — Other specified functional intestinal disorders.
Is K22.0 billable?
- Yes. K22.0 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can K22.0 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict K22.0 as a principal diagnosis.
Is K22.0 a CC or MCC?
- No. K22.0 is neither a CC nor an MCC under MS-DRG v44.0.