ICD-10-CM 2027
ICD-10 code for Addison-Schilder complex
From the official ICD-10-CM alphabetic index entry “Addison-Schilder complex”. Page updated September 29, 2026.
About coding Addison-Schilder complex
The ICD-10-CM code for Addison-Schilder complex is E71.528 (Other X-linked adrenoleukodystrophy).
Within E71.52, choose E71.528 (Other X-linked adrenoleukodystrophy) only when documentation doesn't support a more specific option: childhood cerebral X-linked adrenoleukodystrophy (E71.520), adolescent X-linked adrenoleukodystrophy (E71.521), Adrenomyeloneuropathy (E71.522) and unspecified type (E71.529).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 642 (Inborn and Other Disorders of Metabolism, relative weight 1.3219), in MDC 10 (Endocrine, Nutritional and Metabolic Diseases and Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about Addison-Schilder complex ICD-10 codes
What is the ICD-10 code for Addison-Schilder complex?
- E71.528 — Other X-linked adrenoleukodystrophy.
Is E71.528 billable?
- Yes. E71.528 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can E71.528 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict E71.528 as a principal diagnosis.
Is E71.528 a CC or MCC?
- E71.528 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.