ICD-10-CM 2027
ICD-10 code for adolescent X-linked adrenoleukodystrophy
From the official ICD-10-CM alphabetic index entry “Adolescent X-linked adrenoleukodystrophy”. Page updated September 29, 2026.
About coding adolescent X-linked adrenoleukodystrophy
The ICD-10-CM code for adolescent X-linked adrenoleukodystrophy is E71.521 (Adolescent X-linked adrenoleukodystrophy).
Within E71.52 (X-linked adrenoleukodystrophy), E71.521 is specifically for adolescent X-linked adrenoleukodystrophy. Related codes cover childhood cerebral X-linked adrenoleukodystrophy (E71.520), Adrenomyeloneuropathy (E71.522), other X-linked adrenoleukodystrophy (E71.528) and unspecified type (E71.529).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 642 (Inborn and Other Disorders of Metabolism, relative weight 1.3219), in MDC 10 (Endocrine, Nutritional and Metabolic Diseases and Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about adolescent X-linked adrenoleukodystrophy ICD-10 codes
What is the ICD-10 code for adolescent X-linked adrenoleukodystrophy?
- E71.521 — Adolescent X-linked adrenoleukodystrophy.
Is E71.521 billable?
- Yes. E71.521 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can E71.521 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict E71.521 as a principal diagnosis.
Is E71.521 a CC or MCC?
- E71.521 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.