ICD-10 code for adrenoleukodystrophy

The ICD-10-CM code for adrenoleukodystrophy is E71.529 (X-linked adrenoleukodystrophy, unspecified type). The official index lists 8 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on E71.529.

Within E71.52, choose E71.529 (unspecified type) only when documentation doesn't support a more specific option: childhood cerebral X-linked adrenoleukodystrophy (E71.520), adolescent X-linked adrenoleukodystrophy (E71.521), Adrenomyeloneuropathy (E71.522) and other X-linked adrenoleukodystrophy (E71.528).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 642 (Inborn and Other Disorders of Metabolism, relative weight 1.3219), in MDC 10 (Endocrine, Nutritional and Metabolic Diseases and Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.