ICD-10-CM 2027
ICD-10 code for Ainhum disease
From the official ICD-10-CM alphabetic index entry “Disease, diseased › ainhum”. Page updated September 29, 2026.
About coding Ainhum disease
The ICD-10-CM code for Ainhum disease is L94.6 (Ainhum).
Within L94 (other localized connective tissue disorders), L94.6 is specifically for Ainhum. Related codes cover localized scleroderma [morphea] (L94.0), linear scleroderma (L94.1), Calcinosis cutis (L94.2), Sclerodactyly (L94.3), Gottron's papules (L94.4), Poikiloderma vasculare atrophicans (L94.5), other specified localized connective tissue disorders (L94.8) and localized connective tissue disorder, unspecified (L94.9).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 867 (Other Infectious and Parasitic Diseases Diagnoses with MCC, relative weight 2.1859), DRG 868 (Other Infectious and Parasitic Diseases Diagnoses with CC, relative weight 1.0235) and DRG 869 (Other Infectious and Parasitic Diseases Diagnoses without CC/MCC, relative weight 0.6787), in MDC 18 (Infectious and Parasitic Diseases, Systemic or Unspecified Sites), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about Ainhum disease ICD-10 codes
What is the ICD-10 code for Ainhum disease?
- L94.6 — Ainhum.
Is L94.6 billable?
- Yes. L94.6 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can L94.6 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict L94.6 as a principal diagnosis.
Is L94.6 a CC or MCC?
- No. L94.6 is neither a CC nor an MCC under MS-DRG v44.0.