ICD-10-CM 2027
ICD-10 code for Amyopathic poikilodermatomyositis
From the official ICD-10-CM alphabetic index entry “Poikilodermatomyositis › amyopathic”. Page updated September 29, 2026.
About coding Amyopathic poikilodermatomyositis
The ICD-10-CM code for Amyopathic poikilodermatomyositis is M33.13 (Other dermatomyositis without myopathy).
Within M33.1, choose M33.13 (without myopathy) only when documentation doesn't support a more specific option: organ involvement unspecified (M33.10), with respiratory involvement (M33.11), with myopathy (M33.12) and with other organ involvement (M33.19).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 545 (Connective Tissue Disorders with MCC, relative weight 2.3892), DRG 546 (Connective Tissue Disorders with CC, relative weight 1.1745) and DRG 547 (Connective Tissue Disorders without CC/MCC, relative weight 0.7526), in MDC 08 (Diseases and Disorders of the Musculoskeletal System and Connective Tissue), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about Amyopathic poikilodermatomyositis ICD-10 codes
What is the ICD-10 code for Amyopathic poikilodermatomyositis?
- M33.13 — Other dermatomyositis without myopathy.
Is M33.13 billable?
- Yes. M33.13 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can M33.13 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict M33.13 as a principal diagnosis.
Is M33.13 a CC or MCC?
- M33.13 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.