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ICD-10-CM 2027

ICD-10 code for aortic atresia

Q23.0

Congenital stenosis of aortic valve

✓ Billable / specificCC — complication/comorbidity

From the official ICD-10-CM alphabetic index entry “Atresia, atretic › aortic (orifice) (valve)”. Page updated September 29, 2026.

About coding aortic atresia

The ICD-10-CM code for aortic atresia is Q23.0 (Congenital stenosis of aortic valve). The official index lists 3 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on Q23.0.

Within Q23 (congenital malformations of aortic and mitral valves), Q23.0 is specifically for congenital stenosis of aortic valve. Related codes cover congenital insufficiency of aortic valve (Q23.1), congenital mitral stenosis (Q23.2), congenital mitral insufficiency (Q23.3), Hypoplastic left heart syndrome (Q23.4), other congenital malformations of aortic and mitral valves (Q23.8) and congenital malformation of aortic and mitral valves, unspecified (Q23.9).

Don't report Q23.0 together with the conditions in its Excludes1 note: congenital stenosis of aortic valve in hypoplastic left heart syndrome (Q23.4), congenital subaortic stenosis (Q24.4) and supravalvular aortic stenosis (congenital) (Q25.3).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

More specific aortic atresia codes (official index)

  • arch Q25.21 — Interruption of aortic arch
  • congenital with hypoplasia of ascending aorta and defective development of left ventricle (with mitral stenosis) Q23.4 — Hypoplastic left heart syndrome
  • in hypoplastic left heart syndrome Q23.4 — Hypoplastic left heart syndrome

Don't confuse with (Excludes1 for Q23.0)

  • congenital stenosis of aortic valve in hypoplastic left heart syndrome (Q23.4)
  • congenital subaortic stenosis (Q24.4)
  • supravalvular aortic stenosis (congenital) (Q25.3)

Common questions about aortic atresia ICD-10 codes

What is the ICD-10 code for aortic atresia?

Q23.0 — Congenital stenosis of aortic valve. More specific codes apply when the documentation supports them: Q25.21, Q23.4, Q23.4.

What is the ICD-10 code for arch aortic atresia?

Q25.21 — Interruption of aortic arch.

Is Q23.0 billable?

Yes. Q23.0 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).

Can Q23.0 be used as a principal diagnosis?

Yes. The Medicare Code Editor doesn't restrict Q23.0 as a principal diagnosis.

Is Q23.0 a CC or MCC?

Q23.0 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.