ICD-10-CM 2027
ICD-10 code for benign familial polycythemia
From the official ICD-10-CM alphabetic index entry “Polycythemia (secondary) › benign (familial)”. Page updated September 29, 2026.
About coding benign familial polycythemia
The ICD-10-CM code for benign familial polycythemia is D75.0 (Familial erythrocytosis).
Within D75 (other and unspecified diseases of blood and blood-forming organs), D75.0 is specifically for familial erythrocytosis. Related codes cover secondary polycythemia (D75.1), other specified diseases of blood and blood-forming organs (D75.8), disease of blood and blood-forming organs, unspecified (D75.9) and glucose-6-phosphate dehydrogenase (G6PD) deficiency without anemia (D75.A).
Don't report D75.0 together with the conditions in its Excludes1 note: hereditary ovalocytosis (D58.1).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
Don't confuse with (Excludes1 for D75.0)
- hereditary ovalocytosis (D58.1)
Common questions about benign familial polycythemia ICD-10 codes
What is the ICD-10 code for benign familial polycythemia?
- D75.0 — Familial erythrocytosis.
Is D75.0 billable?
- Yes. D75.0 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can D75.0 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict D75.0 as a principal diagnosis.
Is D75.0 a CC or MCC?
- No. D75.0 is neither a CC nor an MCC under MS-DRG v44.0.