ICD-10 code for bile duct malformation

The ICD-10-CM code for bile duct malformation is Q44.5 (Other congenital malformations of bile ducts).

Within Q44, choose Q44.5 (Other congenital malformations of bile ducts) only when documentation doesn't support a more specific option: agenesis, aplasia and hypoplasia of gallbladder (Q44.0), other congenital malformations of gallbladder (Q44.1), atresia of bile ducts (Q44.2), congenital stenosis and stricture of bile ducts (Q44.3), Choledochal cyst (Q44.4), cystic disease of liver (Q44.6) and other congenital malformations of liver (Q44.7).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 441 (Disorders of Liver Except Malignancy, Cirrhosis or Alcoholic Hepatitis with MCC, relative weight 1.8219), DRG 442 (Disorders of Liver Except Malignancy, Cirrhosis or Alcoholic Hepatitis with CC, relative weight 0.9602) and DRG 443 (Disorders of Liver Except Malignancy, Cirrhosis or Alcoholic Hepatitis without CC/MCC, relative weight 0.6885), in MDC 07 (Diseases and Disorders of the Hepatobiliary System and Pancreas), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.