ICD-10-CM 2027
ICD-10 code for cardiovascular collagenosis
Other cardiomyopathies not elsewhere classified
From the official ICD-10-CM alphabetic index entry “Collagenosis, collagen disease (nonvascular) (vascular) › cardiovascular”. Page updated September 29, 2026.
About coding cardiovascular collagenosis
The ICD-10-CM code for cardiovascular collagenosis is I42.89 (Other cardiomyopathies not elsewhere classified).
Within I42.8 (other cardiomyopathies), I42.89 is specifically for other cardiomyopathies not elsewhere classified. Related codes cover Arrhythmogenic cardiomyopathy (I42.81).
Code first: pre-existing cardiomyopathy complicating pregnancy and puerperium (O99.4).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
Common questions about cardiovascular collagenosis ICD-10 codes
What is the ICD-10 code for cardiovascular collagenosis?
- I42.89 — Other cardiomyopathies not elsewhere classified.
Is I42.89 billable?
- Yes. I42.89 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can I42.89 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict I42.89 as a principal diagnosis.
Is I42.89 a CC or MCC?
- I42.89 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.