ICD-10-CM 2027
ICD-10 code for carnitine metabolism disorder
From the official ICD-10-CM alphabetic index entry “Disorder (of) › carnitine metabolism”. Page updated September 29, 2026.
About coding carnitine metabolism disorder
The ICD-10-CM code for carnitine metabolism disorder is E71.40 (Disorder of carnitine metabolism, unspecified).
Within E71.4, choose E71.40 (Disorder of carnitine metabolism, unspecified) only when documentation doesn't support a more specific option: primary carnitine deficiency (E71.41), carnitine deficiency due to inborn errors of metabolism (E71.42), iatrogenic carnitine deficiency (E71.43) and other secondary carnitine deficiency (E71.44).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 642 (Inborn and Other Disorders of Metabolism, relative weight 1.3219), in MDC 10 (Endocrine, Nutritional and Metabolic Diseases and Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about carnitine metabolism disorder ICD-10 codes
What is the ICD-10 code for carnitine metabolism disorder?
- E71.40 — Disorder of carnitine metabolism, unspecified.
Is E71.40 billable?
- Yes. E71.40 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can E71.40 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict E71.40 as a principal diagnosis.
Is E71.40 a CC or MCC?
- No. E71.40 is neither a CC nor an MCC under MS-DRG v44.0.