ICD-10-CM 2027
ICD-10 code for carotid body paraganglioma
From the official ICD-10-CM alphabetic index entry “Paraganglioma › carotid body”. Page updated September 29, 2026.
About coding carotid body paraganglioma
The ICD-10-CM code for carotid body paraganglioma is D44.6 (Neoplasm of uncertain behavior of carotid body). The official index lists 1 more specific code, so check the documentation for details such as type, cause, site or severity before settling on D44.6.
Within D44 (neoplasm of uncertain behavior of endocrine glands), D44.6 is specifically for neoplasm of uncertain behavior of carotid body. Related codes cover thyroid gland (D44.0), adrenal gland (D44.1), parathyroid gland (D44.2), pituitary gland (D44.3), craniopharyngeal duct (D44.4), pineal gland (D44.5), aortic body and other paraganglia (D44.7) and unspecified endocrine gland (D44.9).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 054 (Nervous System Neoplasms with MCC, relative weight 1.5194) and DRG 055 (Nervous System Neoplasms without MCC, relative weight 1.0296), in MDC 01 (Diseases and Disorders of the Nervous System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
More specific carotid body paraganglioma codes (official index)
- malignant C75.4 — Malignant neoplasm of carotid body
Common questions about carotid body paraganglioma ICD-10 codes
What is the ICD-10 code for carotid body paraganglioma?
- D44.6 — Neoplasm of uncertain behavior of carotid body. More specific codes apply when the documentation supports them: C75.4.
What is the ICD-10 code for malignant carotid body paraganglioma?
- C75.4 — Malignant neoplasm of carotid body.
Is D44.6 billable?
- Yes. D44.6 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can D44.6 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict D44.6 as a principal diagnosis.
Is D44.6 a CC or MCC?
- No. D44.6 is neither a CC nor an MCC under MS-DRG v44.0.