ICD-10-CM 2027
ICD-10 code for Castleman disease
From the official ICD-10-CM alphabetic index entry “Disease, diseased › Castleman (unicentric) (multicentric)”. Page updated September 29, 2026.
About coding Castleman disease
The ICD-10-CM code for Castleman disease is D47.Z2 (Castleman disease). The official index lists 1 more specific code, so check the documentation for details such as type, cause, site or severity before settling on D47.Z2.
Within D47.Z (other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue), D47.Z2 is specifically for Castleman disease. Related codes cover Post-transplant lymphoproliferative disorder (PTLD) (D47.Z1) and other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue (D47.Z9).
The conditions in its Excludes2 note aren't part of D47.Z2, but may be coded alongside it if the patient has both: Kaposi's sarcoma (C46.-).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
More specific Castleman disease codes (official index)
- HHV-8-associated D47.Z2 — Castleman disease
Common questions about Castleman disease ICD-10 codes
What is the ICD-10 code for Castleman disease?
- D47.Z2 — Castleman disease. More specific codes apply when the documentation supports them: D47.Z2.
What is the ICD-10 code for hhv-8-associated castleman disease?
- D47.Z2 — Castleman disease.
Is D47.Z2 billable?
- Yes. D47.Z2 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can D47.Z2 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict D47.Z2 as a principal diagnosis.
Is D47.Z2 a CC or MCC?
- D47.Z2 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.