ICD-10 code for centronuclear myopathy

The ICD-10-CM code for centronuclear myopathy is G71.228 (Other centronuclear myopathy). The official index lists 2 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on G71.228.

Within G71.22, choose G71.228 (Other centronuclear myopathy) only when documentation doesn't support a more specific option: X-linked myotubular myopathy (G71.220).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 091 (Other Disorders of Nervous System with MCC, relative weight 1.7046), DRG 092 (Other Disorders of Nervous System with CC, relative weight 1.0239) and DRG 093 (Other Disorders of Nervous System without CC/MCC, relative weight 0.7783), in MDC 01 (Diseases and Disorders of the Nervous System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.