ICD-10-CM 2027
ICD-10 code for Chiari's disease
From the official ICD-10-CM alphabetic index entry “Disease, diseased › Chiari's (hepatic vein thrombosis)”. Page updated September 29, 2026.
About coding Chiari's disease
The ICD-10-CM code for Chiari's disease is I82.0 (Budd-Chiari syndrome).
Within I82 (other venous embolism and thrombosis), I82.0 is specifically for Budd-Chiari syndrome. Related codes cover thrombophlebitis migrans (I82.1), embolism and thrombosis of vena cava and other thoracic veins (I82.2), embolism and thrombosis of renal vein (I82.3), acute embolism and thrombosis of deep veins of lower extremity (I82.4), chronic embolism and thrombosis of deep veins of lower extremity (I82.5), acute embolism and thrombosis of veins of upper extremity (I82.6), chronic embolism and thrombosis of veins of upper extremity (I82.7), embolism and thrombosis of other specified veins (I82.8) and 4 more.
Code first venous embolism and thrombosis complicating: abortion, ectopic or molar pregnancy (O00-O07, O08.7) and pregnancy, childbirth and the puerperium (O22.-, O87.-).
As a secondary diagnosis it is an MCC (major complication or comorbidity), which can move an inpatient stay into the highest-paying "with MCC" MS-DRG of its family, unless the principal diagnosis excludes it.
Common questions about Chiari's disease ICD-10 codes
What is the ICD-10 code for Chiari's disease?
- I82.0 — Budd-Chiari syndrome.
Is I82.0 billable?
- Yes. I82.0 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can I82.0 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict I82.0 as a principal diagnosis.
Is I82.0 a CC or MCC?
- I82.0 is an MCC (major complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.