ICD-10 code for Churg-Strauss syndrome

The ICD-10-CM code for Churg-Strauss syndrome is M30.1 (Polyarteritis with lung involvement [Churg-Strauss]).

Within M30 (polyarteritis nodosa and related conditions), M30.1 is specifically for polyarteritis with lung involvement [Churg-Strauss]. Related codes cover polyarteritis nodosa (M30.0), juvenile polyarteritis (M30.2), mucocutaneous lymph node syndrome [Kawasaki] (M30.3) and other conditions related to polyarteritis nodosa (M30.8).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 542 (Pathological Fractures and Musculoskeletal and Connective Tissue Malignancy with MCC, relative weight 1.7211), DRG 543 (Pathological Fractures and Musculoskeletal and Connective Tissue Malignancy with CC, relative weight 1.006) and DRG 544 (Pathological Fractures and Musculoskeletal and Connective Tissue Malignancy without CC/MCC, relative weight 0.7406), in MDC 08 (Diseases and Disorders of the Musculoskeletal System and Connective Tissue), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.