ICD-10-CM 2027
ICD-10 code for congenital deafness
From the official ICD-10-CM alphabetic index entry “Deafness (acquired) (complete) (hereditary) (partial) › congenital”. Page updated September 29, 2026.
About coding congenital deafness
The ICD-10-CM code for congenital deafness is H90.5 (Unspecified sensorineural hearing loss). The official index lists 1 more specific code, so check the documentation for details such as type, cause, site or severity before settling on H90.5.
Within H90, choose H90.5 (Unspecified sensorineural hearing loss) only when documentation doesn't support a more specific option: conductive hearing loss, bilateral (H90.0), conductive hearing loss, unilateral with unrestricted hearing on the contralateral side (H90.1), conductive hearing loss, unspecified (H90.2), sensorineural hearing loss, bilateral (H90.3), sensorineural hearing loss, unilateral with unrestricted hearing on the contralateral side (H90.4), mixed conductive and sensorineural hearing loss, bilateral (H90.6), mixed conductive and sensorineural hearing loss, unilateral with unrestricted hearing on the contralateral side (H90.7), mixed conductive and sensorineural hearing loss, unspecified (H90.8) and 1 more.
Don't report H90.5 together with the conditions in its Excludes1 note: abnormal auditory perception (H93.2-) and psychogenic deafness (F44.6).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
More specific congenital deafness codes (official index)
- with blue sclera and fragility of bone Q78.0 — Osteogenesis imperfecta
Don't confuse with (Excludes1 for H90.5)
Common questions about congenital deafness ICD-10 codes
What is the ICD-10 code for congenital deafness?
- H90.5 — Unspecified sensorineural hearing loss. More specific codes apply when the documentation supports them: Q78.0.
Is H90.5 billable?
- Yes. H90.5 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can H90.5 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict H90.5 as a principal diagnosis.
Is H90.5 a CC or MCC?
- No. H90.5 is neither a CC nor an MCC under MS-DRG v44.0.