ICD-10-CM 2027
ICD-10 code for cornea hereditary dystrophy
From the official ICD-10-CM alphabetic index entry “Dystrophy, dystrophia › cornea (hereditary)”. Page updated September 29, 2026.
About coding cornea hereditary dystrophy
The ICD-10-CM code for cornea hereditary dystrophy is H18.50 (Unspecified hereditary corneal dystrophies). The official index lists 6 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on H18.50.
Within H18.5, choose H18.50 (Unspecified hereditary corneal dystrophies) only when documentation doesn't support a more specific option: Endothelial corneal dystrophy (H18.51), epithelial (juvenile) corneal dystrophy (H18.52), Granular corneal dystrophy (H18.53), Lattice corneal dystrophy (H18.54), macular corneal dystrophy (H18.55) and other hereditary corneal dystrophies (H18.59).
To report this condition, pick the subcode that matches the documentation: H18.501 (right eye), H18.502 (left eye), H18.503 (bilateral) and H18.509 (unspecified eye).
It has been part of ICD-10-CM since the code set took effect on October 1, 2015, and changed in FY2021 (expanded into subcodes).
More specific cornea hereditary dystrophy codes (official index)
- endothelial H18.51 — Endothelial corneal dystrophy
- epithelial H18.52 — Epithelial (juvenile) corneal dystrophy
- granular H18.53 — Granular corneal dystrophy
- lattice H18.54 — Lattice corneal dystrophy
- macular H18.55 — Macular corneal dystrophy
- specified type NEC H18.59 — Other hereditary corneal dystrophies
Common questions about cornea hereditary dystrophy ICD-10 codes
What is the ICD-10 code for cornea hereditary dystrophy?
- H18.50 — Unspecified hereditary corneal dystrophies (a header code; report a more specific subcode). More specific codes apply when the documentation supports them: H18.51, H18.52, H18.53, H18.54 and others below.
What is the ICD-10 code for endothelial cornea hereditary dystrophy?
- H18.51 — Endothelial corneal dystrophy (header code; choose a more specific subcode).
What is the ICD-10 code for epithelial cornea hereditary dystrophy?
- H18.52 — Epithelial (juvenile) corneal dystrophy (header code; choose a more specific subcode).
What is the ICD-10 code for granular cornea hereditary dystrophy?
- H18.53 — Granular corneal dystrophy (header code; choose a more specific subcode).
What is the ICD-10 code for lattice cornea hereditary dystrophy?
- H18.54 — Lattice corneal dystrophy (header code; choose a more specific subcode).
What is the ICD-10 code for macular cornea hereditary dystrophy?
- H18.55 — Macular corneal dystrophy (header code; choose a more specific subcode).
Is H18.50 billable?
- No. H18.50 is a header code. Report one of its more specific subcodes instead.