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ICD-10-CM 2027

ICD-10 code for Cowden syndrome

Choose a code from the options below based on the documentation.

From the official ICD-10-CM alphabetic index entry “Syndrome › Cowden”. Page updated September 29, 2026.

About coding Cowden syndrome

The official ICD-10-CM index doesn't give a single default code for cowden syndrome; the code depends on the details below.

More specific Cowden syndrome codes (official index)

  • PTEN related Q85.81 — PTEN hamartoma tumor syndrome
  • specified NEC Q85.82 — Other Cowden syndrome

Common questions about Cowden syndrome ICD-10 codes

What is the ICD-10 code for pten related cowden syndrome?

Q85.81 — PTEN hamartoma tumor syndrome.