ICD-10-CM 2027
ICD-10 code for craniosynostosis
From the official ICD-10-CM alphabetic index entry “Craniosynostosis”. Page updated September 29, 2026.
About coding craniosynostosis
The ICD-10-CM code for craniosynostosis is Q75.009 (Craniosynostosis, unspecified). The official index lists 12 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on Q75.009.
Within Q75.00, choose Q75.009 (unspecified) only when documentation doesn't support a more specific option: type, unilateral (Q75.001) and type, bilateral (Q75.002).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 564 (Other Musculoskeletal System and Connective Tissue Diagnoses with MCC, relative weight 1.4908), DRG 565 (Other Musculoskeletal System and Connective Tissue Diagnoses with CC, relative weight 0.9783) and DRG 566 (Other Musculoskeletal System and Connective Tissue Diagnoses without CC/MCC, relative weight 0.7378), in MDC 08 (Diseases and Disorders of the Musculoskeletal System and Connective Tissue), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
More specific craniosynostosis codes (official index)
- bilateral Q75.002 — Craniosynostosis, unspecified type, bilateral
- coronal Q75.029 — Coronal craniosynostosis, unspecified
- bilateral Q75.022 — Coronal craniosynostosis, bilateral
- unilateral Q75.021 — Coronal craniosynostosis, unilateral
- lambdoid Q75.049 — Lambdoid craniosynostosis, unspecified
- bilateral Q75.042 — Lambdoid craniosynostosis, bilateral
- unilateral Q75.041 — Lambdoid craniosynostosis, unilateral
- metopic Q75.03 — Metopic craniosynostosis
- multi-suture, specified NEC Q75.058 — Other multi-suture craniosynostosis
- sagittal Q75.01 — Sagittal craniosynostosis
- single-suture, specified NEC Q75.08 — Other single-suture craniosynostosis
- unilateral Q75.001 — Craniosynostosis, unspecified type, unilateral
Common questions about craniosynostosis ICD-10 codes
What is the ICD-10 code for craniosynostosis?
- Q75.009 — Craniosynostosis, unspecified. More specific codes apply when the documentation supports them: Q75.002, Q75.029, Q75.022, Q75.021 and others below.
What is the ICD-10 code for bilateral craniosynostosis?
- Q75.002 — Craniosynostosis, unspecified type, bilateral.
What is the ICD-10 code for coronal craniosynostosis?
- Q75.029 — Coronal craniosynostosis, unspecified.
What is the ICD-10 code for lambdoid craniosynostosis?
- Q75.049 — Lambdoid craniosynostosis, unspecified.
What is the ICD-10 code for metopic craniosynostosis?
- Q75.03 — Metopic craniosynostosis.
What is the ICD-10 code for sagittal craniosynostosis?
- Q75.01 — Sagittal craniosynostosis.
What is the ICD-10 code for unilateral craniosynostosis?
- Q75.001 — Craniosynostosis, unspecified type, unilateral.
Is Q75.009 billable?
- Yes. Q75.009 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q75.009 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q75.009 as a principal diagnosis.
Is Q75.009 a CC or MCC?
- No. Q75.009 is neither a CC nor an MCC under MS-DRG v44.0.