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ICD-10-CM 2027

ICD-10 code for dehydrogenase deficiency

Choose a code from the options below based on the documentation.

From the official ICD-10-CM alphabetic index entry “Deficiency, deficient › dehydrogenase”. Page updated September 29, 2026.

About coding dehydrogenase deficiency

The official ICD-10-CM index doesn't give a single default code for dehydrogenase deficiency; the code depends on the details below.

More specific dehydrogenase deficiency codes (official index)

  • long chain/very long chain acyl CoA E71.310 — Long chain/very long chain acyl CoA dehydrogenase deficiency
  • medium chain acyl CoA E71.311 — Medium chain acyl CoA dehydrogenase deficiency
  • short chain acyl CoA E71.312 — Short chain acyl CoA dehydrogenase deficiency

Common questions about dehydrogenase deficiency ICD-10 codes

What is the ICD-10 code for medium chain acyl coa dehydrogenase deficiency?

E71.311 — Medium chain acyl CoA dehydrogenase deficiency.

What is the ICD-10 code for short chain acyl coa dehydrogenase deficiency?

E71.312 — Short chain acyl CoA dehydrogenase deficiency.