ICD-10 code for Dentinogenesis imperfecta

The ICD-10-CM code for Dentinogenesis imperfecta is K00.5 (Hereditary disturbances in tooth structure, not elsewhere classified).

Within K00 (disorders of tooth development and eruption), K00.5 is specifically for hereditary disturbances in tooth structure, not elsewhere classified. Related codes cover Anodontia (K00.0), Supernumerary teeth (K00.1), abnormalities of size and form of teeth (K00.2), Mottled teeth (K00.3), disturbances in tooth formation (K00.4), disturbances in tooth eruption (K00.6), Teething syndrome (K00.7), other disorders of tooth development (K00.8) and 1 more.

It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.

In MS-DRG v44.0, it is part of the grouping logic for DRG 011 (Tracheostomy for Face, Mouth and Neck Diagnoses or Laryngectomy with MCC, relative weight 5.6154), DRG 012 (Tracheostomy for Face, Mouth and Neck Diagnoses or Laryngectomy with CC, relative weight 4.381), DRG 013 (Tracheostomy for Face, Mouth and Neck Diagnoses or Laryngectomy without CC/MCC, relative weight 2.7307), DRG 157 (Dental and Oral Diseases with MCC, relative weight 1.809), DRG 158 (Dental and Oral Diseases with CC, relative weight 0.9366) and DRG 159 (Dental and Oral Diseases without CC/MCC, relative weight 0.6893), in Pre-MDC and MDC 03 (Diseases and Disorders of the Ear, Nose, Mouth and Throat), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.