ICD-10-CM 2027
ICD-10 code for Devergie's disease
From the official ICD-10-CM alphabetic index entry “Devergie's disease (pityriasis rubra pilaris)”. Page updated September 29, 2026.
About coding Devergie's disease
The ICD-10-CM code for Devergie's disease is L44.0 (Pityriasis rubra pilaris).
Within L44 (other papulosquamous disorders), L44.0 is specifically for pityriasis rubra pilaris. Related codes cover lichen nitidus (L44.1), lichen striatus (L44.2), lichen ruber moniliformis (L44.3), infantile papular acrodermatitis [Gianotti-Crosti] (L44.4), other specified papulosquamous disorders (L44.8) and papulosquamous disorder, unspecified (L44.9).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 606 (Minor Skin Disorders with MCC, relative weight 1.5728) and DRG 607 (Minor Skin Disorders without MCC, relative weight 0.8772), in MDC 09 (Diseases and Disorders of the Skin, Subcutaneous Tissue and Breast), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about Devergie's disease ICD-10 codes
What is the ICD-10 code for Devergie's disease?
- L44.0 — Pityriasis rubra pilaris.
Is L44.0 billable?
- Yes. L44.0 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can L44.0 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict L44.0 as a principal diagnosis.
Is L44.0 a CC or MCC?
- No. L44.0 is neither a CC nor an MCC under MS-DRG v44.0.