ICD-10-CM 2027
ICD-10 code for Diamond-Blackfan anemia
Constitutional (pure) red blood cell aplasia
From the official ICD-10-CM alphabetic index entry “Diamond-Blackfan anemia (congenital hypoplastic)”. Page updated September 29, 2026.
About coding Diamond-Blackfan anemia
The ICD-10-CM code for Diamond-Blackfan anemia is D61.01 (Constitutional (pure) red blood cell aplasia).
Within D61.0 (constitutional aplastic anemia), D61.01 is specifically for constitutional (pure) red blood cell aplasia. Related codes cover Shwachman-Diamond syndrome (D61.02), Fanconi anemia (D61.03) and other constitutional aplastic anemia (D61.09).
Don't report D61.01 together with the conditions in its Excludes1 note: acquired red cell aplasia (D60.9).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
Don't confuse with (Excludes1 for D61.01)
- acquired red cell aplasia (D60.9)
Common questions about Diamond-Blackfan anemia ICD-10 codes
What is the ICD-10 code for Diamond-Blackfan anemia?
- D61.01 — Constitutional (pure) red blood cell aplasia.
Is D61.01 billable?
- Yes. D61.01 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can D61.01 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict D61.01 as a principal diagnosis.
Is D61.01 a CC or MCC?
- D61.01 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.