ICD-10 code for dysautonomia

The ICD-10-CM code for dysautonomia is G90.1 (Familial dysautonomia [Riley-Day]).

Within G90 (disorders of autonomic nervous system), G90.1 is specifically for familial dysautonomia [Riley-Day]. Related codes cover idiopathic peripheral autonomic neuropathy (G90.0), Horner's syndrome (G90.2), Multi-system degeneration of the autonomic nervous system (G90.3), autonomic dysreflexia (G90.4), complex regional pain syndrome I (CRPS I) (G90.5), other disorders of autonomic nervous system (G90.8), disorder of the autonomic nervous system, unspecified (G90.9), postural orthostatic tachycardia syndrome [POTS] (G90.A) and 1 more.

It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.

In MS-DRG v44.0, it is part of the grouping logic for DRG 091 (Other Disorders of Nervous System with MCC, relative weight 1.7046), DRG 092 (Other Disorders of Nervous System with CC, relative weight 1.0239), DRG 093 (Other Disorders of Nervous System without CC/MCC, relative weight 0.7783), DRG 791 (Prematurity with Major Problems, relative weight 4.1075) and DRG 793 (Full Term Neonate with Major Problems, relative weight 4.2195), in MDC 01 (Diseases and Disorders of the Nervous System) and MDC 15 (Newborns and Other Neonates with Conditions Originating in the Perinatal Period), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.