ICD-10-CM 2027
ICD-10 code for ear agenesis
From the official ICD-10-CM alphabetic index entry “Agenesis › ear”. Page updated September 29, 2026.
About coding ear agenesis
The ICD-10-CM code for ear agenesis is Q16.9 (Congenital malformation of ear causing impairment of hearing, unspecified). The official index lists 2 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on Q16.9.
Within Q16, choose Q16.9 (Congenital malformation of ear causing impairment of hearing, unspecified) only when documentation doesn't support a more specific option: congenital absence of (ear) auricle (Q16.0), congenital absence, atresia and stricture of auditory canal (external) (Q16.1), absence of eustachian tube (Q16.2), congenital malformation of ear ossicles (Q16.3), other congenital malformations of middle ear (Q16.4) and congenital malformation of inner ear (Q16.5).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 154 (Other Ear, Nose, Mouth and Throat Diagnoses with MCC, relative weight 1.5921), DRG 155 (Other Ear, Nose, Mouth and Throat Diagnoses with CC, relative weight 0.9322) and DRG 156 (Other Ear, Nose, Mouth and Throat Diagnoses without CC/MCC, relative weight 0.6659), in MDC 03 (Diseases and Disorders of the Ear, Nose, Mouth and Throat), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
More specific ear agenesis codes (official index)
Common questions about ear agenesis ICD-10 codes
What is the ICD-10 code for ear agenesis?
- Q16.9 — Congenital malformation of ear causing impairment of hearing, unspecified. More specific codes apply when the documentation supports them: Q16.0, Q17.8.
What is the ICD-10 code for auricle ear agenesis?
- Q16.0 — Congenital absence of (ear) auricle.
What is the ICD-10 code for lobe ear agenesis?
- Q17.8 — Other specified congenital malformations of ear.
Is Q16.9 billable?
- Yes. Q16.9 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q16.9 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q16.9 as a principal diagnosis.
Is Q16.9 a CC or MCC?
- No. Q16.9 is neither a CC nor an MCC under MS-DRG v44.0.