ICD-10-CM 2027
ICD-10 code for essential thrombocythemia
From the official ICD-10-CM alphabetic index entry “Thrombocythemia (hemorrhagic) › essential”. Page updated September 29, 2026.
About coding essential thrombocythemia
The ICD-10-CM code for essential thrombocythemia is D47.3 (Essential (hemorrhagic) thrombocythemia).
Within D47 (other neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue), D47.3 is specifically for essential (hemorrhagic) thrombocythemia. Related codes cover mast cell neoplasms of uncertain behavior (D47.0), chronic myeloproliferative disease (D47.1), monoclonal gammopathy (D47.2), Osteomyelofibrosis (D47.4), neoplasm of uncertain behavior of lymphoid, hematopoietic and related tissue, unspecified (D47.9) and other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue (D47.Z).
The conditions in its Excludes2 note aren't part of D47.3, but may be coded alongside it if the patient has both: reactive thrombocytosis (D75.838), secondary thrombocytosis (D75.838), thrombocythemia NOS (D75.839) and thrombocytosis NOS (D75.839).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
Common questions about essential thrombocythemia ICD-10 codes
What is the ICD-10 code for essential thrombocythemia?
- D47.3 — Essential (hemorrhagic) thrombocythemia.
Is D47.3 billable?
- Yes. D47.3 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can D47.3 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict D47.3 as a principal diagnosis.
Is D47.3 a CC or MCC?
- No. D47.3 is neither a CC nor an MCC under MS-DRG v44.0.