ICD-10-CM 2027
ICD-10 code for Evans syndrome
From the official ICD-10-CM alphabetic index entry “Evans syndrome”. Page updated September 29, 2026.
About coding Evans syndrome
The ICD-10-CM code for Evans syndrome is D69.41 (Evans syndrome).
Within D69.4 (other primary thrombocytopenia), D69.41 is specifically for Evans syndrome. Related codes cover congenital and hereditary thrombocytopenia purpura (D69.42) and other primary thrombocytopenia (D69.49).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 813 (Coagulation Disorders, relative weight 1.5257), in MDC 16 (Diseases and Disorders of the Blood and Blood Forming Organs and Immunological Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about Evans syndrome ICD-10 codes
What is the ICD-10 code for Evans syndrome?
- D69.41 — Evans syndrome.
Is D69.41 billable?
- Yes. D69.41 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can D69.41 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict D69.41 as a principal diagnosis.
Is D69.41 a CC or MCC?
- D69.41 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.