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ICD-10-CM 2027

ICD-10 code for familial aldosteronism

E26.02

Glucocorticoid-remediable aldosteronism

✓ Billable / specific

From the official ICD-10-CM alphabetic index entry “Aldosteronism › familial (type I)”. Page updated September 29, 2026.

About coding familial aldosteronism

The ICD-10-CM code for familial aldosteronism is E26.02 (Glucocorticoid-remediable aldosteronism).

Within E26.0 (primary hyperaldosteronism), E26.02 is specifically for Glucocorticoid-remediable aldosteronism. Related codes cover Conn's syndrome (E26.01) and other primary hyperaldosteronism (E26.09).

It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.

In MS-DRG v44.0, it is part of the grouping logic for DRG 643 (Endocrine Disorders with MCC, relative weight 1.6139), DRG 644 (Endocrine Disorders with CC, relative weight 1.0044) and DRG 645 (Endocrine Disorders without CC/MCC, relative weight 0.7459), in MDC 10 (Endocrine, Nutritional and Metabolic Diseases and Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

Common questions about familial aldosteronism ICD-10 codes

What is the ICD-10 code for familial aldosteronism?

E26.02 — Glucocorticoid-remediable aldosteronism.

Is E26.02 billable?

Yes. E26.02 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).

Can E26.02 be used as a principal diagnosis?

Yes. The Medicare Code Editor doesn't restrict E26.02 as a principal diagnosis.

Is E26.02 a CC or MCC?

No. E26.02 is neither a CC nor an MCC under MS-DRG v44.0.