ICD-10-CM 2027
ICD-10 code for Fanconi anemia
From the official ICD-10-CM alphabetic index entry “Fanconi ('s) anemia”. Page updated September 29, 2026.
About coding Fanconi anemia
The ICD-10-CM code for Fanconi anemia is D61.03 (Fanconi anemia).
Within D61.0 (constitutional aplastic anemia), D61.03 is specifically for Fanconi anemia. Related codes cover constitutional (pure) red blood cell aplasia (D61.01), Shwachman-Diamond syndrome (D61.02) and other constitutional aplastic anemia (D61.09).
Don't report D61.03 together with the conditions in its Excludes1 note: Fanconi syndrome (E72.0-).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
Don't confuse with (Excludes1 for D61.03)
- Fanconi syndrome (E72.0-)
Common questions about Fanconi anemia ICD-10 codes
What is the ICD-10 code for Fanconi anemia?
- D61.03 — Fanconi anemia.
Is D61.03 billable?
- Yes. D61.03 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can D61.03 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict D61.03 as a principal diagnosis.
Is D61.03 a CC or MCC?
- D61.03 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.