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ICD-10-CM 2027

ICD-10 code for Fanconi anemia

D61.03

Fanconi anemia

✓ Billable / specificCC — complication/comorbidity

From the official ICD-10-CM alphabetic index entry “Fanconi ('s) anemia”. Page updated September 29, 2026.

About coding Fanconi anemia

The ICD-10-CM code for Fanconi anemia is D61.03 (Fanconi anemia).

Within D61.0 (constitutional aplastic anemia), D61.03 is specifically for Fanconi anemia. Related codes cover constitutional (pure) red blood cell aplasia (D61.01), Shwachman-Diamond syndrome (D61.02) and other constitutional aplastic anemia (D61.09).

Don't report D61.03 together with the conditions in its Excludes1 note: Fanconi syndrome (E72.0-).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

Don't confuse with (Excludes1 for D61.03)

Common questions about Fanconi anemia ICD-10 codes

What is the ICD-10 code for Fanconi anemia?

D61.03 — Fanconi anemia.

Is D61.03 billable?

Yes. D61.03 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).

Can D61.03 be used as a principal diagnosis?

Yes. The Medicare Code Editor doesn't restrict D61.03 as a principal diagnosis.

Is D61.03 a CC or MCC?

D61.03 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.