ICD-10-CM 2027
ICD-10 code for fatty acid disorder
Choose a code from the options below based on the documentation.
From the official ICD-10-CM alphabetic index entry “Disorder (of) › fatty acid”. Page updated September 29, 2026.
About coding fatty acid disorder
The official ICD-10-CM index doesn't give a single default code for fatty acid disorder; the code depends on the details below.
More specific fatty acid disorder codes (official index)
- metabolism E71.30 — Disorder of fatty-acid metabolism, unspecified
- specified NEC E71.39 — Other disorders of fatty-acid metabolism
- oxidation
- LCAD E71.310 — Long chain/very long chain acyl CoA dehydrogenase deficiency
- MCAD E71.311 — Medium chain acyl CoA dehydrogenase deficiency
- SCAD E71.312 — Short chain acyl CoA dehydrogenase deficiency
- specified deficiency NEC E71.318 — Other disorders of fatty-acid oxidation
Common questions about fatty acid disorder ICD-10 codes
What is the ICD-10 code for metabolism fatty acid disorder?
- E71.30 — Disorder of fatty-acid metabolism, unspecified.