ICD-10-CM 2027
ICD-10 code for fetalis ichthyosis
From the official ICD-10-CM alphabetic index entry “Ichthyosis (congenital) › fetalis”. Page updated September 29, 2026.
About coding fetalis ichthyosis
The ICD-10-CM code for fetalis ichthyosis is Q80.4 (Harlequin fetus).
Within Q80 (congenital ichthyosis), Q80.4 is specifically for Harlequin fetus. Related codes cover ichthyosis vulgaris (Q80.0), X-linked ichthyosis (Q80.1), lamellar ichthyosis (Q80.2), congenital bullous ichthyosiform erythroderma (Q80.3), other congenital ichthyosis (Q80.8) and unspecified (Q80.9).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 606 (Minor Skin Disorders with MCC, relative weight 1.5728) and DRG 607 (Minor Skin Disorders without MCC, relative weight 0.8772), in MDC 09 (Diseases and Disorders of the Skin, Subcutaneous Tissue and Breast), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about fetalis ichthyosis ICD-10 codes
What is the ICD-10 code for fetalis ichthyosis?
- Q80.4 — Harlequin fetus.
Is Q80.4 billable?
- Yes. Q80.4 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q80.4 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q80.4 as a principal diagnosis.
Is Q80.4 a CC or MCC?
- No. Q80.4 is neither a CC nor an MCC under MS-DRG v44.0.