ICD-10 code for Fontan related circulation

The ICD-10-CM code for Fontan related circulation is I27.849 (Fontan related circulation, unspecified). The official index lists 3 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on I27.849.

Within I27.84, choose I27.849 (unspecified) only when documentation doesn't support a more specific option: Fontan-associated liver disease [FALD] (I27.840), Fontan-associated lymphatic dysfunction (I27.841) and other Fontan-associated condition (I27.848).

It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.

In MS-DRG v44.0, it is part of the grouping logic for DRG 314 (Other Circulatory System Diagnoses with MCC, relative weight 2.0873), DRG 315 (Other Circulatory System Diagnoses with CC, relative weight 0.9508) and DRG 316 (Other Circulatory System Diagnoses without CC/MCC, relative weight 0.6677), in MDC 05 (Diseases and Disorders of the Circulatory System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.