ICD-10 code for Hallervorden-Spatz disease

The ICD-10-CM code for Hallervorden-Spatz disease is G23.0 (Hallervorden-Spatz disease).

Within G23 (other degenerative diseases of basal ganglia), G23.0 is specifically for Hallervorden-Spatz disease. Related codes cover progressive supranuclear ophthalmoplegia [Steele-Richardson-Olszewski] (G23.1), Striatonigral degeneration (G23.2), Hypomyelination with atrophy of the basal ganglia and cerebellum (G23.3), other specified degenerative diseases of basal ganglia (G23.8) and degenerative disease of basal ganglia, unspecified (G23.9).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 056 (Degenerative Nervous System Disorders with MCC, relative weight 2.2655) and DRG 057 (Degenerative Nervous System Disorders without MCC, relative weight 1.2838), in MDC 01 (Diseases and Disorders of the Nervous System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.