ICD-10-CM 2027
ICD-10 code for hemochromatosis
From the official ICD-10-CM alphabetic index entry “Hemochromatosis”. Page updated September 29, 2026.
About coding hemochromatosis
The ICD-10-CM code for hemochromatosis is E83.119 (Hemochromatosis, unspecified). The official index lists 6 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on E83.119.
Within E83.11, choose E83.119 (unspecified) only when documentation doesn't support a more specific option: hereditary hemochromatosis (E83.110), due to repeated red blood cell transfusions (E83.111) and other hemochromatosis (E83.118).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 642 (Inborn and Other Disorders of Metabolism, relative weight 1.3219), in MDC 10 (Endocrine, Nutritional and Metabolic Diseases and Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
More specific hemochromatosis codes (official index)
- with refractory anemia D46.1 — Refractory anemia with ring sideroblasts
- due to repeated red blood cell transfusion E83.111 — Hemochromatosis due to repeated red blood cell transfusions
- hereditary (primary) E83.110 — Hereditary hemochromatosis
- neonatal P78.84 — Gestational alloimmune liver disease
- primary E83.110 — Hereditary hemochromatosis
- specified NEC E83.118 — Other hemochromatosis
Common questions about hemochromatosis ICD-10 codes
What is the ICD-10 code for hemochromatosis?
- E83.119 — Hemochromatosis, unspecified. More specific codes apply when the documentation supports them: D46.1, E83.111, E83.110, P78.84 and others below.
What is the ICD-10 code for hereditary hemochromatosis?
- E83.110 — Hereditary hemochromatosis.
What is the ICD-10 code for neonatal hemochromatosis?
- P78.84 — Gestational alloimmune liver disease.
What is the ICD-10 code for primary hemochromatosis?
- E83.110 — Hereditary hemochromatosis.
Is E83.119 billable?
- Yes. E83.119 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can E83.119 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict E83.119 as a principal diagnosis.
Is E83.119 a CC or MCC?
- No. E83.119 is neither a CC nor an MCC under MS-DRG v44.0.