ICD-10-CM 2027
ICD-10 code for ichthyosis
From the official ICD-10-CM alphabetic index entry “Ichthyosis (congenital)”. Page updated September 29, 2026.
About coding ichthyosis
The ICD-10-CM code for ichthyosis is Q80.9 (Congenital ichthyosis, unspecified). The official index lists 10 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on Q80.9.
Within Q80, choose Q80.9 (unspecified) only when documentation doesn't support a more specific option: ichthyosis vulgaris (Q80.0), X-linked ichthyosis (Q80.1), lamellar ichthyosis (Q80.2), congenital bullous ichthyosiform erythroderma (Q80.3), Harlequin fetus (Q80.4) and other congenital ichthyosis (Q80.8).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 606 (Minor Skin Disorders with MCC, relative weight 1.5728) and DRG 607 (Minor Skin Disorders without MCC, relative weight 0.8772), in MDC 09 (Diseases and Disorders of the Skin, Subcutaneous Tissue and Breast), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
More specific ichthyosis codes (official index)
- acquired L85.0 — Acquired ichthyosis
- fetalis Q80.4 — Harlequin fetus
- hystrix Q80.8 — Other congenital ichthyosis
- lamellar Q80.2 — Lamellar ichthyosis
- lingual K13.29 — Other disturbances of oral epithelium, including tongue
- palmaris and plantaris Q82.8 — Other specified congenital malformations of skin
- simplex Q80.0 — Ichthyosis vulgaris
- vera Q80.8 — Other congenital ichthyosis
- vulgaris Q80.0 — Ichthyosis vulgaris
- X-linked Q80.1 — X-linked ichthyosis
Common questions about ichthyosis ICD-10 codes
What is the ICD-10 code for ichthyosis?
- Q80.9 — Congenital ichthyosis, unspecified. More specific codes apply when the documentation supports them: L85.0, Q80.4, Q80.8, Q80.2 and others below.
What is the ICD-10 code for acquired ichthyosis?
- L85.0 — Acquired ichthyosis.
What is the ICD-10 code for fetalis ichthyosis?
- Q80.4 — Harlequin fetus.
What is the ICD-10 code for hystrix ichthyosis?
- Q80.8 — Other congenital ichthyosis.
What is the ICD-10 code for lamellar ichthyosis?
- Q80.2 — Lamellar ichthyosis.
What is the ICD-10 code for lingual ichthyosis?
- K13.29 — Other disturbances of oral epithelium, including tongue.
What is the ICD-10 code for palmaris and plantaris ichthyosis?
- Q82.8 — Other specified congenital malformations of skin.
Is Q80.9 billable?
- Yes. Q80.9 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q80.9 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q80.9 as a principal diagnosis.
Is Q80.9 a CC or MCC?
- No. Q80.9 is neither a CC nor an MCC under MS-DRG v44.0.