ICD-10-CM 2027
ICD-10 code for ileum agenesis
Congenital absence, atresia and stenosis of ileum
From the official ICD-10-CM alphabetic index entry “Agenesis › ileum”. Page updated September 29, 2026.
About coding ileum agenesis
The ICD-10-CM code for ileum agenesis is Q41.2 (Congenital absence, atresia and stenosis of ileum).
Within Q41 (congenital absence, atresia and stenosis of small intestine), Q41.2 is specifically for congenital absence, atresia and stenosis of ileum. Related codes cover duodenum (Q41.0), jejunum (Q41.1), other specified parts of small intestine (Q41.8) and part unspecified (Q41.9).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 393 (Other Digestive System Diagnoses with MCC, relative weight 1.5881), DRG 394 (Other Digestive System Diagnoses with CC, relative weight 0.9228) and DRG 395 (Other Digestive System Diagnoses without CC/MCC, relative weight 0.6382), in MDC 06 (Diseases and Disorders of the Digestive System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about ileum agenesis ICD-10 codes
What is the ICD-10 code for ileum agenesis?
- Q41.2 — Congenital absence, atresia and stenosis of ileum.
Is Q41.2 billable?
- Yes. Q41.2 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q41.2 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q41.2 as a principal diagnosis.
Is Q41.2 a CC or MCC?
- Q41.2 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.