ICD-10-CM 2027
ICD-10 code for intestinal lipodystrophy
From the official ICD-10-CM alphabetic index entry “Lipodystrophy › intestinal”. Page updated September 29, 2026.
About coding intestinal lipodystrophy
The ICD-10-CM code for intestinal lipodystrophy is K90.81 (Whipple's disease).
Within K90.8 (other intestinal malabsorption), K90.81 is specifically for Whipple's disease. Related codes cover short bowel syndrome (K90.82), intestinal failure (K90.83) and other intestinal malabsorption (K90.89).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 393 (Other Digestive System Diagnoses with MCC, relative weight 1.5881), DRG 394 (Other Digestive System Diagnoses with CC, relative weight 0.9228) and DRG 395 (Other Digestive System Diagnoses without CC/MCC, relative weight 0.6382), in MDC 06 (Diseases and Disorders of the Digestive System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about intestinal lipodystrophy ICD-10 codes
What is the ICD-10 code for intestinal lipodystrophy?
- K90.81 — Whipple's disease.
Is K90.81 billable?
- Yes. K90.81 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can K90.81 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict K90.81 as a principal diagnosis.
Is K90.81 a CC or MCC?
- K90.81 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.