ICD-10-CM 2027
ICD-10 code for Kayser-Fleischer ring
From the official ICD-10-CM alphabetic index entry “Kayser-Fleischer ring (cornea) (pseudosclerosis)”. Page updated September 29, 2026.
About coding Kayser-Fleischer ring
The ICD-10-CM code for Kayser-Fleischer ring is H18.04 (Kayser-Fleischer ring).
Within H18.0 (corneal pigmentations and deposits), H18.04 is specifically for Kayser-Fleischer ring. Related codes cover unspecified corneal deposit (H18.00), anterior corneal pigmentations (H18.01), Argentous corneal deposits (H18.02), corneal deposits in metabolic disorders (H18.03), posterior corneal pigmentations (H18.05) and stromal corneal pigmentations (H18.06).
To report this condition, pick the subcode that matches the documentation: H18.041 (right eye), H18.042 (left eye), H18.043 (bilateral) and H18.049 (unspecified eye).
It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.