ICD-10-CM 2027
ICD-10 code for Klippel-Feil deficiency
From the official ICD-10-CM alphabetic index entry “Klippel-Feil deficiency, disease, or syndrome (brevicollis)”. Page updated September 29, 2026.
About coding Klippel-Feil deficiency
The ICD-10-CM code for Klippel-Feil deficiency is Q76.1 (Klippel-Feil syndrome).
Within Q76 (congenital malformations of spine and bony thorax), Q76.1 is specifically for Klippel-Feil syndrome. Related codes cover spina bifida occulta (Q76.0), congenital spondylolisthesis (Q76.2), congenital scoliosis due to congenital bony malformation (Q76.3), other congenital malformations of spine, not associated with scoliosis (Q76.4), cervical rib (Q76.5), other congenital malformations of ribs (Q76.6), congenital malformation of sternum (Q76.7), other congenital malformations of bony thorax (Q76.8) and 1 more.
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 564 (Other Musculoskeletal System and Connective Tissue Diagnoses with MCC, relative weight 1.4908), DRG 565 (Other Musculoskeletal System and Connective Tissue Diagnoses with CC, relative weight 0.9783) and DRG 566 (Other Musculoskeletal System and Connective Tissue Diagnoses without CC/MCC, relative weight 0.7378), in MDC 08 (Diseases and Disorders of the Musculoskeletal System and Connective Tissue), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about Klippel-Feil deficiency ICD-10 codes
What is the ICD-10 code for Klippel-Feil deficiency?
- Q76.1 — Klippel-Feil syndrome.
Is Q76.1 billable?
- Yes. Q76.1 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q76.1 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q76.1 as a principal diagnosis.
Is Q76.1 a CC or MCC?
- No. Q76.1 is neither a CC nor an MCC under MS-DRG v44.0.