ICD-10-CM 2027
ICD-10 code for kwashiorkor
From the official ICD-10-CM alphabetic index entry “Kwashiorkor”. Page updated September 29, 2026.
About coding kwashiorkor
The ICD-10-CM code for kwashiorkor is E40 (Kwashiorkor). The official index lists 1 more specific code, so check the documentation for details such as type, cause, site or severity before settling on E40.
Don't report E40 together with the conditions in its Excludes1 note: marasmic kwashiorkor (E42).
As a secondary diagnosis it is an MCC (major complication or comorbidity), which can move an inpatient stay into the highest-paying "with MCC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 640 (Miscellaneous Disorders of Nutrition, Metabolism, Fluids and Electrolytes with MCC, relative weight 1.3395) and DRG 641 (Miscellaneous Disorders of Nutrition, Metabolism, Fluids and Electrolytes without MCC, relative weight 0.7865), in MDC 10 (Endocrine, Nutritional and Metabolic Diseases and Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
More specific kwashiorkor codes (official index)
- marasmic, marasmus type E42 — Marasmic kwashiorkor
Don't confuse with (Excludes1 for E40)
- marasmic kwashiorkor (E42)
Common questions about kwashiorkor ICD-10 codes
What is the ICD-10 code for kwashiorkor?
- E40 — Kwashiorkor. More specific codes apply when the documentation supports them: E42.
Is E40 billable?
- Yes. E40 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can E40 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict E40 as a principal diagnosis.
Is E40 a CC or MCC?
- E40 is an MCC (major complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.