ICD-10-CM 2027
ICD-10 code for lichenoides pityriasis
From the official ICD-10-CM alphabetic index entry “Pityriasis (capitis) › lichenoides”. Page updated September 29, 2026.
About coding lichenoides pityriasis
The ICD-10-CM code for lichenoides pityriasis is L41.0 (Pityriasis lichenoides et varioliformis acuta). The official index lists 2 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on L41.0.
Within L41 (parapsoriasis), L41.0 is specifically for pityriasis lichenoides et varioliformis acuta. Related codes cover pityriasis lichenoides chronica (L41.1), small plaque parapsoriasis (L41.3), large plaque parapsoriasis (L41.4), Retiform parapsoriasis (L41.5), other parapsoriasis (L41.8) and unspecified (L41.9).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 595 (Major Skin Disorders with MCC, relative weight 2.0239) and DRG 596 (Major Skin Disorders without MCC, relative weight 1.1071), in MDC 09 (Diseases and Disorders of the Skin, Subcutaneous Tissue and Breast), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
More specific lichenoides pityriasis codes (official index)
Common questions about lichenoides pityriasis ICD-10 codes
What is the ICD-10 code for lichenoides pityriasis?
- L41.0 — Pityriasis lichenoides et varioliformis acuta. More specific codes apply when the documentation supports them: L41.1, L41.0.
What is the ICD-10 code for chronica lichenoides pityriasis?
- L41.1 — Pityriasis lichenoides chronica.
What is the ICD-10 code for et varioliformis lichenoides pityriasis?
- L41.0 — Pityriasis lichenoides et varioliformis acuta.
Is L41.0 billable?
- Yes. L41.0 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can L41.0 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict L41.0 as a principal diagnosis.
Is L41.0 a CC or MCC?
- No. L41.0 is neither a CC nor an MCC under MS-DRG v44.0.