ICD-10-CM 2027
ICD-10 code for linear scleroderma
From the official ICD-10-CM alphabetic index entry “Scleroderma, sclerodermia (acrosclerotic) (diffuse) (generalized) (progressive) (pulmonary) › linear”. Page updated September 29, 2026.
About coding linear scleroderma
The ICD-10-CM code for linear scleroderma is L94.1 (Linear scleroderma).
Within L94 (other localized connective tissue disorders), L94.1 is specifically for linear scleroderma. Related codes cover localized scleroderma [morphea] (L94.0), Calcinosis cutis (L94.2), Sclerodactyly (L94.3), Gottron's papules (L94.4), Poikiloderma vasculare atrophicans (L94.5), Ainhum (L94.6), other specified localized connective tissue disorders (L94.8) and localized connective tissue disorder, unspecified (L94.9).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 606 (Minor Skin Disorders with MCC, relative weight 1.5728) and DRG 607 (Minor Skin Disorders without MCC, relative weight 0.8772), in MDC 09 (Diseases and Disorders of the Skin, Subcutaneous Tissue and Breast), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about linear scleroderma ICD-10 codes
What is the ICD-10 code for linear scleroderma?
- L94.1 — Linear scleroderma.
Is L94.1 billable?
- Yes. L94.1 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can L94.1 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict L94.1 as a principal diagnosis.
Is L94.1 a CC or MCC?
- No. L94.1 is neither a CC nor an MCC under MS-DRG v44.0.