ICD-10-CM 2027
ICD-10 code for lip malformation
From the official ICD-10-CM alphabetic index entry “Malformation (congenital) › lip”. Page updated September 29, 2026.
About coding lip malformation
The ICD-10-CM code for lip malformation is Q38.0 (Congenital malformations of lips, not elsewhere classified).
Within Q38 (other congenital malformations of tongue, mouth and pharynx), Q38.0 is specifically for congenital malformations of lips, not elsewhere classified. Related codes cover Ankyloglossia (Q38.1), Macroglossia (Q38.2), other congenital malformations of tongue (Q38.3), congenital malformations of salivary glands and ducts (Q38.4), congenital malformations of palate, not elsewhere classified (Q38.5), other congenital malformations of mouth (Q38.6), congenital pharyngeal pouch (Q38.7) and other congenital malformations of pharynx (Q38.8).
Don't report Q38.0 together with the conditions in its Excludes1 note: cleft lip (Q36.-), cleft lip with cleft palate (Q37.-), macrocheilia (Q18.6) and microcheilia (Q18.7).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
Don't confuse with (Excludes1 for Q38.0)
Common questions about lip malformation ICD-10 codes
What is the ICD-10 code for lip malformation?
- Q38.0 — Congenital malformations of lips, not elsewhere classified.
Is Q38.0 billable?
- Yes. Q38.0 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q38.0 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q38.0 as a principal diagnosis.
Is Q38.0 a CC or MCC?
- No. Q38.0 is neither a CC nor an MCC under MS-DRG v44.0.