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ICD-10-CM 2027

ICD-10 code for lipoprotein disorder

Choose a code from the options below based on the documentation.

From the official ICD-10-CM alphabetic index entry “Disorder (of) › lipoprotein”. Page updated September 29, 2026.

About coding lipoprotein disorder

The official ICD-10-CM index doesn't give a single default code for lipoprotein disorder; the code depends on the details below.

More specific lipoprotein disorder codes (official index)

  • deficiency (familial) E78.6 — Lipoprotein deficiency
  • metabolism E78.9 — Disorder of lipoprotein metabolism, unspecified
  • specified NEC E78.89 — Other lipoprotein metabolism disorders

Common questions about lipoprotein disorder ICD-10 codes

What is the ICD-10 code for deficiency lipoprotein disorder?

E78.6 — Lipoprotein deficiency.

What is the ICD-10 code for metabolism lipoprotein disorder?

E78.9 — Disorder of lipoprotein metabolism, unspecified.