ICD-10-CM 2027
ICD-10 code for Lymphangiomyoma
From the official ICD-10-CM alphabetic index entry “Lymphangiomyoma”. Page updated September 29, 2026.
About coding Lymphangiomyoma
The ICD-10-CM code for Lymphangiomyoma is D18.1 (Lymphangioma, any site).
Within D18 (Hemangioma and lymphangioma, any site), D18.1 is specifically for lymphangioma, any site. Related codes cover Hemangioma (D18.0).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 814 (Reticuloendothelial and Immunity Disorders with MCC, relative weight 2.0729), DRG 815 (Reticuloendothelial and Immunity Disorders with CC, relative weight 1.0444) and DRG 816 (Reticuloendothelial and Immunity Disorders without CC/MCC, relative weight 0.7381), in MDC 16 (Diseases and Disorders of the Blood and Blood Forming Organs and Immunological Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about Lymphangiomyoma ICD-10 codes
What is the ICD-10 code for Lymphangiomyoma?
- D18.1 — Lymphangioma, any site.
Is D18.1 billable?
- Yes. D18.1 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can D18.1 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict D18.1 as a principal diagnosis.
Is D18.1 a CC or MCC?
- No. D18.1 is neither a CC nor an MCC under MS-DRG v44.0.