ICD-10-CM 2027
ICD-10 code for Meckel-Gruber syndrome
From the official ICD-10-CM alphabetic index entry “Meckel-Gruber syndrome”. Page updated September 29, 2026.
About coding Meckel-Gruber syndrome
The ICD-10-CM code for Meckel-Gruber syndrome is Q61.9 (Cystic kidney disease, unspecified).
Within Q61, choose Q61.9 (unspecified) only when documentation doesn't support a more specific option: congenital renal cyst (Q61.0), polycystic kidney, infantile type (Q61.1), polycystic kidney, adult type (Q61.2), polycystic kidney, unspecified (Q61.3), renal dysplasia (Q61.4), medullary cystic kidney (Q61.5) and other cystic kidney diseases (Q61.8).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 698 (Other Kidney and Urinary Tract Diagnoses with MCC, relative weight 1.6398), DRG 699 (Other Kidney and Urinary Tract Diagnoses with CC, relative weight 1.0003) and DRG 700 (Other Kidney and Urinary Tract Diagnoses without CC/MCC, relative weight 0.6741), in MDC 11 (Diseases and Disorders of the Kidney and Urinary Tract), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about Meckel-Gruber syndrome ICD-10 codes
What is the ICD-10 code for Meckel-Gruber syndrome?
- Q61.9 — Cystic kidney disease, unspecified.
Is Q61.9 billable?
- Yes. Q61.9 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q61.9 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q61.9 as a principal diagnosis.
Is Q61.9 a CC or MCC?
- Q61.9 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.