ICD-10-CM 2027
ICD-10 code for Megaloesophagus
From the official ICD-10-CM alphabetic index entry “Megaloesophagus (functional)”. Page updated September 29, 2026.
About coding Megaloesophagus
The ICD-10-CM code for Megaloesophagus is K22.0 (Achalasia of cardia). The official index lists 1 more specific code, so check the documentation for details such as type, cause, site or severity before settling on K22.0.
Within K22 (other diseases of esophagus), K22.0 is specifically for Achalasia of cardia. Related codes cover ulcer of esophagus (K22.1), esophageal obstruction (K22.2), perforation of esophagus (K22.3), dyskinesia of esophagus (K22.4), diverticulum of esophagus, acquired (K22.5), Gastro-esophageal laceration-hemorrhage syndrome (K22.6), Barrett's esophagus (K22.7), other specified diseases of esophagus (K22.8) and 1 more.
Don't report K22.0 together with the conditions in its Excludes1 note: congenital cardiospasm (Q39.5).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
More specific Megaloesophagus codes (official index)
- congenital Q39.5 — Congenital dilatation of esophagus
Don't confuse with (Excludes1 for K22.0)
- congenital cardiospasm (Q39.5)
Common questions about Megaloesophagus ICD-10 codes
What is the ICD-10 code for Megaloesophagus?
- K22.0 — Achalasia of cardia. More specific codes apply when the documentation supports them: Q39.5.
What is the ICD-10 code for congenital megaloesophagus?
- Q39.5 — Congenital dilatation of esophagus.
Is K22.0 billable?
- Yes. K22.0 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can K22.0 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict K22.0 as a principal diagnosis.
Is K22.0 a CC or MCC?
- No. K22.0 is neither a CC nor an MCC under MS-DRG v44.0.