ICD-10-CM 2027
ICD-10 code for Methylmalonic acidemia
From the official ICD-10-CM alphabetic index entry “Acidemia › methylmalonic”. Page updated September 29, 2026.
About coding Methylmalonic acidemia
The ICD-10-CM code for Methylmalonic acidemia is E71.120 (Methylmalonic acidemia).
Within E71.12 (disorders of propionate metabolism), E71.120 is specifically for Methylmalonic acidemia. Related codes cover propionic acidemia (E71.121) and other disorders of propionate metabolism (E71.128).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 642 (Inborn and Other Disorders of Metabolism, relative weight 1.3219), in MDC 10 (Endocrine, Nutritional and Metabolic Diseases and Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about Methylmalonic acidemia ICD-10 codes
What is the ICD-10 code for Methylmalonic acidemia?
- E71.120 — Methylmalonic acidemia.
Is E71.120 billable?
- Yes. E71.120 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can E71.120 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict E71.120 as a principal diagnosis.
Is E71.120 a CC or MCC?
- E71.120 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.